Table 6.13.1 Open in new tab Clinical... | Oxford Academic

Table 6.13.1

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Clinical frequencies and mean ages at diagnosis of the major complications of von Hippel–Lindau disease (3)

Lesion	Prevalence n = 52	Mean age at diagnosis^a
Retinal angioma	89 (59%)	25.4 ± 12.7 years (Range: 4–68 years)
Cerebellar haemangioblastoma	89 (59%)	29.0 ± 10.0 years (Range: 13–61 years)
Spinal cord haemangioblastoma	20 (13%)	33.9 ± 12.6 years (Range: 11–60 years)
Renal cell carcinoma	43 (28%)	44.0 ± 10.9 years (Range: from 16 years)
Phaeochromocytoma	11 (7%)	20.2 ± 7.6 years (Range: 12–36 years)

Lesion	Prevalence n = 52	Mean age at diagnosis^a
Retinal angioma	89 (59%)	25.4 ± 12.7 years (Range: 4–68 years)
Cerebellar haemangioblastoma	89 (59%)	29.0 ± 10.0 years (Range: 13–61 years)
Spinal cord haemangioblastoma	20 (13%)	33.9 ± 12.6 years (Range: 11–60 years)
Renal cell carcinoma	43 (28%)	44.0 ± 10.9 years (Range: from 16 years)
Phaeochromocytoma	11 (7%)	20.2 ± 7.6 years (Range: 12–36 years)

^a

Includes both symptomatic and presymptomatic diagnoses.