| Variables . | N = 137 . |
|---|---|
| Male, n (%) | 80 (58.4%) |
| Anatomical diagnosis | |
| Right ventricle dominant | 60 (43.8%) |
| Heterotaxy | 24 (17.5%) |
| HLHS | 13 (9.5%) |
| Double outlet right ventricle | 6 (4.4%) |
| Single ventricle | 5 (3.6%) |
| TGA | 3 (2.2%) |
| Unbalanced atrioventricular septal defect | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| ccTGA | 2 (1.5%) |
| Shone’s complex | 2 (1.5%) |
| Left ventricle dominant | 68 (49.6%) |
| Tricuspid atresia | 22 (16.1%) |
| PA/IVS | 18 (13.1%) |
| Single ventricle | 11 (8.0%) |
| TGA, hypoplastic right ventricle | 5 (3.6%) |
| Heterotaxy | 3 (2.2%) |
| Double outlet right ventricle | 2 (1.5%) |
| Others | 7 (5.1%) |
| Two ventricles/intermediate | 9 (6.6%) |
| Double outlet right ventricle | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| Heterotaxy | 2 (1.5%) |
| Others | 2 (1.5%) |
| Post-TAPVC repair | 14 (10.2%) |
| Age at the Fontan operation (years) | 2.3 (1.6–3.6) |
| Body weight at the Fontan operation (kg) | 10.9 (9.1–12.8) |
| Extracardiac TCPC | 136 (99.3%) |
| Lateral tunnel TCPC | 1 (0.7%) |
| Fenestrated TCPC | 81 (59.1%) |
| Conduit size of extracardiac TCPC | |
| 12 mm | 1 (0.73%) |
| 14 mm | 5 (3.6%) |
| 16 mm | 117 (85.4%) |
| 18 mm | 13 (9.5%) |
| Pre-Fontan procedures | |
| Blalock–Thomas–Taussig shunt | 64 (46.7%) |
| Pulmonary artery banding | 52 (38.0%) |
| Norwood procedure | 21 (15.3%) |
| Pulmonary artery plasty | 15 (10.9%) |
| SVC pressure at pre-Fontan (mmHg) | 11 (10–12) |
| Central venous pressure at pre-Fontan (mmHg) | 6 (4–8) |
| Variables . | N = 137 . |
|---|---|
| Male, n (%) | 80 (58.4%) |
| Anatomical diagnosis | |
| Right ventricle dominant | 60 (43.8%) |
| Heterotaxy | 24 (17.5%) |
| HLHS | 13 (9.5%) |
| Double outlet right ventricle | 6 (4.4%) |
| Single ventricle | 5 (3.6%) |
| TGA | 3 (2.2%) |
| Unbalanced atrioventricular septal defect | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| ccTGA | 2 (1.5%) |
| Shone’s complex | 2 (1.5%) |
| Left ventricle dominant | 68 (49.6%) |
| Tricuspid atresia | 22 (16.1%) |
| PA/IVS | 18 (13.1%) |
| Single ventricle | 11 (8.0%) |
| TGA, hypoplastic right ventricle | 5 (3.6%) |
| Heterotaxy | 3 (2.2%) |
| Double outlet right ventricle | 2 (1.5%) |
| Others | 7 (5.1%) |
| Two ventricles/intermediate | 9 (6.6%) |
| Double outlet right ventricle | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| Heterotaxy | 2 (1.5%) |
| Others | 2 (1.5%) |
| Post-TAPVC repair | 14 (10.2%) |
| Age at the Fontan operation (years) | 2.3 (1.6–3.6) |
| Body weight at the Fontan operation (kg) | 10.9 (9.1–12.8) |
| Extracardiac TCPC | 136 (99.3%) |
| Lateral tunnel TCPC | 1 (0.7%) |
| Fenestrated TCPC | 81 (59.1%) |
| Conduit size of extracardiac TCPC | |
| 12 mm | 1 (0.73%) |
| 14 mm | 5 (3.6%) |
| 16 mm | 117 (85.4%) |
| 18 mm | 13 (9.5%) |
| Pre-Fontan procedures | |
| Blalock–Thomas–Taussig shunt | 64 (46.7%) |
| Pulmonary artery banding | 52 (38.0%) |
| Norwood procedure | 21 (15.3%) |
| Pulmonary artery plasty | 15 (10.9%) |
| SVC pressure at pre-Fontan (mmHg) | 11 (10–12) |
| Central venous pressure at pre-Fontan (mmHg) | 6 (4–8) |
Data are presented as median interquartile range or frequency (%).
BCPC: bidirectional cavopulmonary connection; ccTGA: congenitally corrected transposition of the great arteries; HLHS: hypoplastic left heart syndrome; PA/IVS: pulmonary atresia with intact ventricular septum; TGA: transposition of the great arteries; TAPVC: total anomalous pulmonary venous connection; TCPC: total cavopulmonary connection; VSD: ventricular septal defect.
| Variables . | N = 137 . |
|---|---|
| Male, n (%) | 80 (58.4%) |
| Anatomical diagnosis | |
| Right ventricle dominant | 60 (43.8%) |
| Heterotaxy | 24 (17.5%) |
| HLHS | 13 (9.5%) |
| Double outlet right ventricle | 6 (4.4%) |
| Single ventricle | 5 (3.6%) |
| TGA | 3 (2.2%) |
| Unbalanced atrioventricular septal defect | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| ccTGA | 2 (1.5%) |
| Shone’s complex | 2 (1.5%) |
| Left ventricle dominant | 68 (49.6%) |
| Tricuspid atresia | 22 (16.1%) |
| PA/IVS | 18 (13.1%) |
| Single ventricle | 11 (8.0%) |
| TGA, hypoplastic right ventricle | 5 (3.6%) |
| Heterotaxy | 3 (2.2%) |
| Double outlet right ventricle | 2 (1.5%) |
| Others | 7 (5.1%) |
| Two ventricles/intermediate | 9 (6.6%) |
| Double outlet right ventricle | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| Heterotaxy | 2 (1.5%) |
| Others | 2 (1.5%) |
| Post-TAPVC repair | 14 (10.2%) |
| Age at the Fontan operation (years) | 2.3 (1.6–3.6) |
| Body weight at the Fontan operation (kg) | 10.9 (9.1–12.8) |
| Extracardiac TCPC | 136 (99.3%) |
| Lateral tunnel TCPC | 1 (0.7%) |
| Fenestrated TCPC | 81 (59.1%) |
| Conduit size of extracardiac TCPC | |
| 12 mm | 1 (0.73%) |
| 14 mm | 5 (3.6%) |
| 16 mm | 117 (85.4%) |
| 18 mm | 13 (9.5%) |
| Pre-Fontan procedures | |
| Blalock–Thomas–Taussig shunt | 64 (46.7%) |
| Pulmonary artery banding | 52 (38.0%) |
| Norwood procedure | 21 (15.3%) |
| Pulmonary artery plasty | 15 (10.9%) |
| SVC pressure at pre-Fontan (mmHg) | 11 (10–12) |
| Central venous pressure at pre-Fontan (mmHg) | 6 (4–8) |
| Variables . | N = 137 . |
|---|---|
| Male, n (%) | 80 (58.4%) |
| Anatomical diagnosis | |
| Right ventricle dominant | 60 (43.8%) |
| Heterotaxy | 24 (17.5%) |
| HLHS | 13 (9.5%) |
| Double outlet right ventricle | 6 (4.4%) |
| Single ventricle | 5 (3.6%) |
| TGA | 3 (2.2%) |
| Unbalanced atrioventricular septal defect | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| ccTGA | 2 (1.5%) |
| Shone’s complex | 2 (1.5%) |
| Left ventricle dominant | 68 (49.6%) |
| Tricuspid atresia | 22 (16.1%) |
| PA/IVS | 18 (13.1%) |
| Single ventricle | 11 (8.0%) |
| TGA, hypoplastic right ventricle | 5 (3.6%) |
| Heterotaxy | 3 (2.2%) |
| Double outlet right ventricle | 2 (1.5%) |
| Others | 7 (5.1%) |
| Two ventricles/intermediate | 9 (6.6%) |
| Double outlet right ventricle | 3 (2.2%) |
| Multiple/large VSD | 2 (1.5%) |
| Heterotaxy | 2 (1.5%) |
| Others | 2 (1.5%) |
| Post-TAPVC repair | 14 (10.2%) |
| Age at the Fontan operation (years) | 2.3 (1.6–3.6) |
| Body weight at the Fontan operation (kg) | 10.9 (9.1–12.8) |
| Extracardiac TCPC | 136 (99.3%) |
| Lateral tunnel TCPC | 1 (0.7%) |
| Fenestrated TCPC | 81 (59.1%) |
| Conduit size of extracardiac TCPC | |
| 12 mm | 1 (0.73%) |
| 14 mm | 5 (3.6%) |
| 16 mm | 117 (85.4%) |
| 18 mm | 13 (9.5%) |
| Pre-Fontan procedures | |
| Blalock–Thomas–Taussig shunt | 64 (46.7%) |
| Pulmonary artery banding | 52 (38.0%) |
| Norwood procedure | 21 (15.3%) |
| Pulmonary artery plasty | 15 (10.9%) |
| SVC pressure at pre-Fontan (mmHg) | 11 (10–12) |
| Central venous pressure at pre-Fontan (mmHg) | 6 (4–8) |
Data are presented as median interquartile range or frequency (%).
BCPC: bidirectional cavopulmonary connection; ccTGA: congenitally corrected transposition of the great arteries; HLHS: hypoplastic left heart syndrome; PA/IVS: pulmonary atresia with intact ventricular septum; TGA: transposition of the great arteries; TAPVC: total anomalous pulmonary venous connection; TCPC: total cavopulmonary connection; VSD: ventricular septal defect.
This PDF is available to Subscribers Only
View Article Abstract & Purchase OptionsFor full access to this pdf, sign in to an existing account, or purchase an annual subscription.
